病因不明性肺纖維化診斷與治療新知 - tsim.org.tw
2013 24 446-452. . . . . (idiopathic pulmonary fibrosis, IPF) . . IPF . (TGF- 1) . (telomere) (glutathione) . . 2011 IPF IPF . . . (corticosteroid) (cyclosporine A) . (INF- 1B) (bosentan) (etanercept) . NAC (N-acetylcysteine) prednisolone azathioprine pirfenidone IPF . IPF . (Idiopathic pulmonary fibrosis). (Usual interstitial pneumonia). (Interstitial pneumonia). (cryptogenic fibrosing alveolitis CFA) IIP 7 . (idiopathic pulmonary IPF . fibrosis IPF) 1,2 . 2000 IPF (Consensus Statement) . (idiopathic interstitial pneumonia . IIP) . IPF . 553 . 447. 3 (fibroblast) . . 2010 IPF.
病因不明性肺纖維化 447 化,且關乎較差之預後3。美國胸腔醫學會、歐 洲胸腔醫學會、日本胸腔醫學會和拉丁美洲胸
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