脱髄・髄鞘障害性疾患 - UMIN
(major dense line) (intraperiod line) 1a (oligodendrocyte: OLs) (Schwann cell: SCs) OLs SCs SCs (basal lamina) OLs OLs (neural stem cell) (bipolar progenitor) (polydendrocyte) pro-OLs OLs OLs 1c OLs halo 1b (intrafascicular) OLs (satellite) (perineuronal) OLs OLs OLs 1c OLs 2',3'-Cyclic-nucleotide 3'-phosphodiesterase (CNPase) proteolipid protein (PLP)
Acute hemorrhagic leukoencephalitis Viral PML, SSPE, HIV encephalopathy, HIV vacuolar myelopathy, HTLV type I- and II-associated myelopathy (tropical spastic paraplegia) Genetic ALD, AMN, MLD (sulphatide lipidoses), GCL (Krabbe disease, galactosylceramide lipidosis), PMD and related PLP1 mutations, Spongiform leukodystrophy (Canavan disease),
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