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A motor function measure scale for neuromuscular …

A motor function measure scale for neuromuscular and validation studyCarole Be rarda,*, Christine Payanb, Isabelle Hodgkinsona, Jacques Fermanianc,The MFM Collaborative Study GroupaDepartment of Paediatric Rehabilitation, l Escale, Centre Hospitalier Lyon-Sud, 69495 Pierre Be nite, FrancebAFM, Institute of Myology, Ho pital Pitie -Salpe`trie`re, Paris, FrancecDepartment of Biostatistics, Ho pital Necker, Paris, FranceReceived 19 November 2004; received in revised form 7 March 2005; accepted 15 March 2005 AbstractA new scale for motor function measurement has been developed for neuromuscular diseases. The validation study included 303 patients,aged 6 62 years. Seventy-two patients had Duchenne muscular dystrophy, 32 Becker muscular dystrophy, 30 limb-girdle musculardystrophy, 39 facio-scapulo-humeral dystrophy, 29 myotonic dystrophy, 21 congenital myopathy, 10 congenital muscular dystrophy, 35spinal muscular atrophy and 35 hereditary neuropathy.

A motor function measure scale for neuromuscular diseases. Construction and validation study Carole Be´rarda,*, Christine Payanb, …

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  Scale, Validation, Disease, Construction, Measure, Functions, Neuromuscular, Function measure scale for neuromuscular, Function measure scale for neuromuscular diseases, Construction and validation

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