Transcription of IgG4 関連大動脈周囲炎 動脈周囲炎 および後腹膜線維症の診 …
1 - 1 - igg4 / Diagnostic Guidelines for igg4 -related periaortitis/periarteritis and retroperitoneal fibrosis igg4 - 2 - 1. igg4 Immunoglobulin G4 ( igg4 ) igg4 igg4 2001 igg4 igg4 ( igg4 -related disease) igg4 igg4 2017 ( 300) 2. igg4 2011 igg4 (135mg/dL ) ( igg4 ) 3 igg4 igg4 3.
2 / igg4 igg4 igg4 / - 3 - igg4 / igg4 ( ) igg4 ( ) igg4 ( 2) 30 5 28 igg4 - 4 - ( 1) igg4 / 1 CT a.
3 ( ) ( )*1,2,3,4 b. *5 c. ( ) 2. igg4 (135mg/dL ) 3. a. b. *6,7,8 igg4 igg4 10 /hpf igg4 /IgG 40% 30 /hpf igg4 /IgG 40% ) (storiform fibrosis) (obliterative phlebitis) 4. ( ) B. 1. 1(a/b/c)+3a 1(a/b/c)+2+4 2. 3a 1(a/b/c)+3b 1(a/b/c)+4 3. 3b 1(a/b/c)+2 ( / ) *1 ( ) *2 ( ) *3 ( ) Erdheim-Chester *4 ( / ) *5 *6 *7 Elastica van Gieson *8 - 5 - ( 2)
4 ( ) - 6 - ( 3) igg4 / ( 4) igg4 ( ) - 7.
