ICD-10 Codes IMMUNODEFICIENCIES - AAAAI

1 IMMUNODEFICIENCIES DISEASE Codes ICD-10 CM ICD-9 CM D71 FUNCTIONAL DISORDERS OF POLYMORPHONUCLEAR NEUTROPHILS Applicable To: Cell membrane receptor complex [CR3] defect Chronic (childhood) granulomatous disease Congenital dysphagocytosis Progressive septic granulomatosis D71 is grouped within Diagnostic Related Group(s) (MS-DRG ): 808, 809, 810 D80 IMMUNODEFICIENCY WITH PREDOMINANTLY ANTIBODY DEFECTS Hereditary hypogammaglobulinemia Applicable To: Autosomal recessive agammaglobulinemia (Swiss type) X-linked agammaglobulinemia [Bruton] (with growth hormone deficiency) Nonfamilial hypogammaglobulinemia Applicable To.

2 Agammaglobulinemia with immunoglobulin-bearing B-lymphocytes Common variable agammaglobulinemia [CVAgamma] Hypogammaglobulinemia NOS Selective deficiency of immunoglobulin A [IgA] Selective deficiency of immunoglobulin G [IgG] subclasses Selective deficiency of immunoglobulin M [IgM] Immunodeficiency with increased immunoglobulin M [IgM] D80 to are grouped within Diagnostic Related Group(s) (MS-DRG ): 814, 815, 816 Antibody deficiency with near-normal immunoglobulins or with hyperimmunoglobulinemia is grouped within Diagnostic Related Group(s) (MS-DRG ): 808, 809 810 Transient hypogammaglobulinemia of infancy is grouped within Diagnostic Related Group(s) (MS-DRG ): 814, 815, 816 Other IMMUNODEFICIENCIES with predominantly antibody defects Applicable To.

3 Kappa light chain deficiency Immunodeficiency with predominantly antibody defects, unspecified and are grouped within Diagnostic Related Group(s) (MS-DRG ): 808, 809 810 D81 COMBINED IMMUNODEFICIENCIES Severe combined immunodeficiency [SCID] with reticular dysgenesis Severe combined immunodeficiency [SCID] with low T- and B-cell numbers Severe combined immunodeficiency [SCID] with low or normal B-cell numbers to are grouped within Diagnostic Related Group(s) (MS-DRG ): 808, 809 810 Adenosine deaminase [ADA] deficiency is grouped within Diagnostic Related Group (MS-DRG ).

4 642 Nezelof's syndrome is grouped within Diagnostic Related Group(s) (MS-DRG ): 808, 809 810 Purine nucleoside phosphorylase [PNP] deficiency is grouped within Diagnostic Related Group (MS-DRG ): 642 Major histocompatibility complex class I deficiency Applicable To: Bare lymphocyte syndrome Major histocompatibility complex class II deficiency and are grouped within Diagnostic Related Group(s) (MS-DRG ): 808, 809 810 OTHER COMBINED IMMUNODEFICIENCIES Biotin-dependent carboxylase deficiency (not billable, use one of the below Codes ) Biotinidase deficiency is grouped within Diagnostic Related Group (MS-DRG ): 642 Other biotin-dependent carboxylase deficiency Applicable To.

5 Holocarboxylase synthetase deficiency Holocarboxylase synthetase deficiency Other biotin-dependent carboxylase deficiency, unspecified Applicable To: Multiple carboxylase deficiency, unspecified and are grouped within Diagnostic Related Group(s) (MS-DRG ): 640, 641 Other combined IMMUNODEFICIENCIES Combined immunodeficiency, unspecified Applicable To: Severe combined immunodeficiency disorder [SCID] NOS and are grouped within Diagnostic Related Group(s) (MS-DRG ): 808, 809, 810 D82 IMMUNODEFICIENCY ASSCIATED WITH OTHER MAJOR DEFECTS Wiskott-Aldrich syndrome Applicable To: Immunodeficiency with thrombocytopenia and eczema Di George's syndrome Applicable To.

6 Pharyngeal pouch syndrome Thymic alymphoplasia Thymic aplasia or hypoplasia with immunodeficiency and are grouped within Diagnostic Related Group(s) (MS-DRG ): 808, 809, 810 Immunodeficiency with short-limbed stature Immunodeficiency following hereditary defective response to Epstein-Barr virus Applicable To: X-linked lymphoproliferative disease Hyperimmunoglobulin E [IgE] syndrome Immunodeficiency associated with other specified major defects Immunodeficiency associated with major defect, unspecified to D are grouped within Diagnostic Related Group(s) (MS-DRG ).

7 814, 815, 816 D83 COMMON VARIABLE IMMUNODEFICIENCY Common variable immunodeficiency with predominant abnormalities of B-cell numbers and function Common variable immunodeficiency with predominant immunoregulatory T-cell disorders Common variable immunodeficiency with autoantibodies to B- or T-cells Other common variable IMMUNODEFICIENCIES Common variable immunodeficiency, unspecified to are grouped within Diagnostic Related Group(s) (MS-DRG ): 814, 815, 816 D84 OTHER IMMUNODEFICIENCIES lymphocyte function antigen-1 [LFA-1] defect is grouped within Diagnostic Related Group(s) (MS-DRG ): 814, 815, 816 Defects in the complement system Applicable To: C1 estrase inhibitor [C1-INH] deficiency (not inherited deficiency in complement components) is grouped within Diagnostic Related Group (MS-DRG ).

8 642 Other specified IMMUNODEFICIENCIES or Immunodeficiency, unspecified and are grouped within Diagnostic Related Group(s) (MS-DRG ): 814, 815, 816 D89 OTHER DISORDERS INVOLVING THE IMMUNE MECHANISM, NOT ELSEWHERE CLASSIFIED Polyclonal hypergammaglobulinemia Applicable To: Benign hypergammaglobulinemic purpura Polyclonal gammopathy NOS is grouped within Diagnostic Related Group(s) (MS-DRG ): 814, 815, 816 Cryoglobulinemia Applicable To: Cryoglobulinemic purpura Cryoglobulinemic vasculitis Essential cryoglobulinemia Idiopathic cryoglobulinemia Mixed cryoglobulinemia Primary cryoglobulinemia Secondary cryoglobulinemia is grouped within Diagnostic Related Group(s) (MS-DRG ): 820 to 825, 840 to 842 Hypergammaglobulinemia, unspecified or Immune reconstitution syndrome Applicable To.

9 Immune reconsitution inflammatory syndrome {IRIS} Use additional code for adverse effect, if applicable to identify drug (T36-T50) with fifth or sixth character 5) and are grouped within Diagnostic Related Group(s) (MS-DRG ): 814, 815, 816 Mast cell activation syndrome and related disorders (not billable, use one of the below Codes ) Mast cell activation, unspecified Applicable To: Mast cell activation disorder, unspecified Mast cell activation syndrome, NOS Monoclonal mast cell activation syndrome Idiopathic mast cell activation syndrome Secondary mast cell activation Applicable To: Secondary mast cell activation syndrome Code also underlying etiology, if known Other mast cell activation disorder Applicable To.

10 Other mast cell activation syndrome to and are grouped within Diagnostic Related Group(s) (MS-DRG ): 814, 815, 816 OTHER SPECIFIED DISORDERS INVOLVING THE IMMUNE MECHANISM, NOT ELSEWHERE CLASSIFIED Graft-versus-host disease (not billable, use one of the below Codes ) Acute graft-versus-host disease Chronic graft-versus-host disease Acute on chronic graft-versus-host disease Graft-versus-host disease, unspecified to are are grouped within Diagnostic Related Group(s) (MS-DRG ): 808, 809, 810