ICD-10 Codes IMMUNODEFICIENCIES - AAAAI

1 IMMUNODEFICIENCIES DISEASE Codes ICD-10 CM ICD-9 CM D71 FUNCTIONAL DISORDERS OF POLYMORPHONUCLEAR NEUTROPHILS Applicable To: Cell membrane receptor complex [CR3] defect Chronic (childhood) granulomatous disease Congenital dysphagocytosis Progressive septic granulomatosis D71 is grouped within Diagnostic Related Group(s) (MS-DRG ): 808, 809, 810 D80 IMMUNODEFICIENCY WITH PREDOMINANTLY ANTIBODY DEFECTS Hereditary hypogammaglobulinemia Applicable To: Autosomal recessive agammaglobulinemia (Swiss type) X-linked agammaglobulinemia [Bruton] (with growth hormone deficiency) Nonfamilial hypogammaglobulinemia Applicable To: Agammaglobulinemia with immunoglobulin-bearing B-lymphocytes Common variable agammaglobulinemia [CVAgamma] Hypogammaglobulinemia NOS Selective deficiency of immunoglobulin A [IgA] Selective deficiency of immunoglobulin G [IgG] subclasses Selective deficiency of immunoglobulin M [IgM] Immunodeficiency with increased immunoglobulin M [IgM] D80 to are grouped within Diagnostic Related Group(s) (MS-DRG ): 814, 815, 816 Antibody deficiency with near-normal immunoglobulins or with hyperimmunoglobulinemia is grouped within Diagnostic Related Group(s) (MS-DRG ): 808, 809 810 Transient hypogammaglobulinemia of infancy is grouped within Diagnostic Related Group(s) (MS-DRG ): 814, 815, 816 Other IMMUNODEFICIENCIES with predominantly antibody defects Applicable To.

2 Kappa light chain deficiency Immunodeficiency with predominantly antibody defects, unspecified and are grouped within Diagnostic Related Group(s) (MS-DRG ): 808, 809 810 D81 COMBINED IMMUNODEFICIENCIES Severe combined immunodeficiency [SCID] with reticular dysgenesis Severe combined immunodeficiency [SCID] with low T- and B-cell numbers Severe combined immunodeficiency [SCID] with low or normal B-cell numbers to are grouped within Diagnostic Related Group(s) (MS-DRG ): 808, 809 810 Adenosine deaminase [ADA] deficiency is grouped within Diagnostic Related Group (MS-DRG ): 642 Nezelof's syndrome is grouped within Diagnostic Related Group(s) (MS-DRG ): 808, 809 810 Purine nucleoside phosphorylase [PNP] deficiency is grouped within Diagnostic Related Group (MS-DRG ): 642 Major histocompatibility complex class I deficiency Applicable To: Bare lymphocyte syndrome Major histocompatibility complex class II deficiency and are grouped within Diagnostic Related Group(s) (MS-DRG ): 808, 809 810 OTHER COMBINED IMMUNODEFICIENCIES Biotin-dependent carboxylase deficiency (not billable, use one of the below Codes ) Biotinidase deficiency is grouped within Diagnostic Related Group (MS-DRG ): 642 Other biotin-dependent carboxylase deficiency Applicable To: Holocarboxylase synthetase deficiency Holocarboxylase synthetase deficiency Other biotin-dependent carboxylase deficiency, unspecified Applicable To: Multiple carboxylase deficiency, unspecified and are grouped within Diagnostic Related Group(s) (MS-DRG ): 640, 641 Other combined IMMUNODEFICIENCIES Combined immunodeficiency, unspecified Applicable To.

3 Severe combined immunodeficiency disorder [SCID] NOS and are grouped within Diagnostic Related Group(s) (MS-DRG ): 808, 809, 810 D82 IMMUNODEFICIENCY ASSCIATED WITH OTHER MAJOR DEFECTS Wiskott-Aldrich syndrome Applicable To: Immunodeficiency with thrombocytopenia and eczema Di George's syndrome Applicable To: Pharyngeal pouch syndrome Thymic alymphoplasia Thymic aplasia or hypoplasia with immunodeficiency and are grouped within Diagnostic Related Group(s) (MS-DRG ): 808, 809, 810 Immunodeficiency with short-limbed stature Immunodeficiency following hereditary defective response to Epstein-Barr virus Applicable To: X-linked lymphoproliferative disease Hyperimmunoglobulin E [IgE] syndrome Immunodeficiency associated with other specified major defects Immunodeficiency associated with major defect, unspecified to D are grouped within Diagnostic Related Group(s) (MS-DRG ): 814, 815, 816 D83 COMMON VARIABLE IMMUNODEFICIENCY Common variable immunodeficiency with predominant abnormalities of B-cell numbers and function Common variable immunodeficiency with predominant immunoregulatory T-cell disorders Common variable immunodeficiency with autoantibodies to B- or T-cells Other common variable IMMUNODEFICIENCIES Common variable immunodeficiency, unspecified to are grouped within Diagnostic Related Group(s) (MS-DRG ): 814, 815, 816 D84 OTHER IMMUNODEFICIENCIES Lymphocyte function antigen-1 [LFA-1] defect is grouped within Diagnostic Related Group(s) (MS-DRG ).

4 814, 815, 816 Defects in the complement system Applicable To: C1 estrase inhibitor [C1-INH] deficiency (not inherited deficiency in complement components) is grouped within Diagnostic Related Group (MS-DRG ): 642 Other specified IMMUNODEFICIENCIES or Immunodeficiency, unspecified and are grouped within Diagnostic Related Group(s) (MS-DRG ): 814, 815, 816 D89 OTHER DISORDERS INVOLVING THE IMMUNE MECHANISM, NOT ELSEWHERE CLASSIFIED Polyclonal hypergammaglobulinemia Applicable To: Benign hypergammaglobulinemic purpura Polyclonal gammopathy NOS is grouped within Diagnostic Related Group(s) (MS-DRG ): 814, 815, 816 Cryoglobulinemia Applicable To: Cryoglobulinemic purpura Cryoglobulinemic vasculitis Essential cryoglobulinemia Idiopathic cryoglobulinemia Mixed cryoglobulinemia Primary cryoglobulinemia Secondary cryoglobulinemia is grouped within Diagnostic Related Group(s) (MS-DRG ): 820 to 825, 840 to 842 Hypergammaglobulinemia, unspecified or Immune reconstitution syndrome Applicable To: Immune reconsitution inflammatory syndrome {IRIS} Use additional code for adverse effect, if applicable to identify drug (T36-T50) with fifth or sixth character 5) and are grouped within Diagnostic Related Group(s) (MS-DRG ): 814, 815, 816 Mast cell activation syndrome and related disorders (not billable, use one of the below Codes ) Mast cell activation, unspecified Applicable To.

5 Mast cell activation disorder, unspecified Mast cell activation syndrome, NOS Monoclonal mast cell activation syndrome Idiopathic mast cell activation syndrome Secondary mast cell activation Applicable To: Secondary mast cell activation syndrome code also underlying etiology, if known Other mast cell activation disorder Applicable To: Other mast cell activation syndrome to and are grouped within Diagnostic Related Group(s) (MS-DRG ): 814, 815, 816 OTHER SPECIFIED DISORDERS INVOLVING THE IMMUNE MECHANISM, NOT ELSEWHERE CLASSIFIED Graft-versus-host disease (not billable, use one of the below Codes ) Acute graft-versus-host disease Chronic graft-versus-host disease Acute on chronic graft-versus-host disease Graft-versus-host disease, unspecified to are are grouped within Diagnostic Related Group(s) (MS-DRG ): 808, 809, 810 Autoimmune lymphoproliferative syndrome [ALPS] is grouped within Diagnostic Related Group(s) (MS-DRG ): 545, 546, 547 Other specified disorders involving the immune mechanism, not elsewhere classified Type 1 Excludes: Human immunodeficiency virus disease (B20) is grouped within Diagnostic Related Group(s) (MS-DRG ): Disorder involving the immune mechanism, unspecified Applicable To.

6 Immune disease NOS is grouped within Diagnostic Related Group(s) (MS-DRG ): 814, 815, 816 3/2017