Transcription of 骨髄増殖性腫瘍 - med.kindai.ac.jp
1 17 - - 4 B NK T / 1 myeloproliferative neoplasms + / 100.
2 Philadelphia ABL BCR Ph1 BCR/ABL BCR-ABL 2 617 95 / 100 2 617 95 ) 85.
3 1 - 2 - - 2 - polycythemia vera
4 PaO2 1 200 400 45 50 60 150 10 15 essential thrombocythemia 100 500 WHO 3 2001 WHO 4 2008 A1 60 A2 B1 B2 B3 B4 B5 A1 45 A2 A3 A4 JAK2V617F
5 A1 A4 1 2 3 1 2 3 4 2014 9 primary myelofibrosis TGF PDGF dry tap Dry tap dry tap 1.
6 2. 3. 1 2 JAK2 JAK ( ) JAK2 2 617 95 2 617 50 30 515 / 5 2 617 50 30 515 / 15