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骨髄増殖性腫瘍 - med.kindai.ac.jp

17 - - 4 B NK T / 1 myeloproliferative neoplasms +

第17回 血液学を学ぼう! 2015.5.11 骨髄増殖性腫瘍-急性骨髄性白血病以外にもある骨髄系腫瘍-

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Transcription of 骨髄増殖性腫瘍 - med.kindai.ac.jp

1 17 - - 4 B NK T / 1 myeloproliferative neoplasms + / 100.

2 Philadelphia ABL BCR Ph1 BCR/ABL BCR-ABL 2 617 95 / 100 2 617 95 ) 85.

3 1 - 2 - - 2 - polycythemia vera

4 PaO2 1 200 400 45 50 60 150 10 15 essential thrombocythemia 100 500 WHO 3 2001 WHO 4 2008 A1 60 A2 B1 B2 B3 B4 B5 A1 45 A2 A3 A4 JAK2V617F

5 A1 A4 1 2 3 1 2 3 4 2014 9 primary myelofibrosis TGF PDGF dry tap Dry tap dry tap 1.

6 2. 3. 1 2 JAK2 JAK ( ) JAK2 2 617 95 2 617 50 30 515 / 5 2 617 50 30 515 / 15


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