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Brugada症候群と診断した女性2例の症例について

brugada . brugada 2 . 1 1 1 1. 1 1 2 2. 2 1. 1 24 16 . 12. brugada . brugada . brugada ICD .. VF . ICD . 2 . 63 . 12 . coved brugada . VF . ICD brugada . brugada 29 . 2 . brugada .. 80 1 2 Chen . brugada brugada SCN5A . SCN5A . Keywords brugada .. brugada . 3 . 1 . 734-8551 1-2-3 brugada 2 . 2 . Two female cases diagosed as brugada syndrome Yukiko Nakano, Hiroshi Ogi, Miwa Miyoshi, Noboru Oda, Kazuyoshi Suenari, Yoshimasa Yamamoto, Kazuaki Chayama, Ken Ishibashi, Aritsune Hirai, Tomokazu Okimoto S-4-26 JPN. J. ELECTROCARDIOLOGY Vol. 26 SUPPL. 4 2006. X.. 1 24 15 brugada . 16 ICD .. 16 7 sinus node dysfunction AV node dysfunction.

S-4-26 JPN. J. ELECTROCARDIOLOGY Vol. 26 SUPPL. 4 2006 Ⅰ.はじめに Brugada症候群の有病率には人種差があり,アジ ア人に多いこと,また性差もありBrugada症候群の

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Transcription of Brugada症候群と診断した女性2例の症例について

1 brugada . brugada 2 . 1 1 1 1. 1 1 2 2. 2 1. 1 24 16 . 12. brugada . brugada . brugada ICD .. VF . ICD . 2 . 63 . 12 . coved brugada . VF . ICD brugada . brugada 29 . 2 . brugada .. 80 1 2 Chen . brugada brugada SCN5A . SCN5A . Keywords brugada .. brugada . 3 . 1 . 734-8551 1-2-3 brugada 2 . 2 . Two female cases diagosed as brugada syndrome Yukiko Nakano, Hiroshi Ogi, Miwa Miyoshi, Noboru Oda, Kazuyoshi Suenari, Yoshimasa Yamamoto, Kazuaki Chayama, Ken Ishibashi, Aritsune Hirai, Tomokazu Okimoto S-4-26 JPN. J. ELECTROCARDIOLOGY Vol. 26 SUPPL. 4 2006. X.. 1 24 15 brugada . 16 ICD .. 16 7 sinus node dysfunction AV node dysfunction.

2 ECG J mm ST baseline . brugada 3 VF . ICD SCN5A . V 1 V 2 type 1 P1090L polymorphism . coved ST .. ST 2 63 17 10 19 . 1 1 .. brugada brugada .. 1 1 . JPN. J. ELECTROCARDIOLOGY Vol. 26 SUPPL. 4 2006 S-4-27. 2 2 .. X 29 26 68 27 . MRI 2 29 brugada . VF 13 8 8 . V1 V2 type . 1 coved 5 1 . ST ST 1 1 . type 3 2 5 brugada type 1 coved sinus node AV node ST 24 ICD . baseline 2 VF 26 1 1 . ICD . J mm ST . 1 .. brugada . brugada . 2 . Ito brugada . 4 . brugada . 5 . S-4-28 JPN. J. ELECTROCARDIOLOGY Vol. 26 SUPPL. 4 2006. Wang Q : Genetic basis and molecular mechanism for 1 Nademanee K, Veerakul G, Nimmannit S, Chaowakul V, idiopathic ventricular fibrillation.

3 Nature, 1998 ; 392 : Bhuripanyo K, Likittanasombat K, Tunsanga K, 293 296. Kuasirikul S, Malasit P, Tansupasawadikul S, 4 Di Diego JM, Cordeiro JM, Goodrow RJ, Fish JM, Tatsanavivat P : Arrhythmogenic marker for the Zygmunt AC, Perez GJ, Scornik FS, Antzelevitch C : sudden unexplained death syndrome in Thai men. Ionic and cellular basis for the predominance of the Circulation, 1997 ; 96 : 2595 2600 brugada syndrome phenotype in males. Circulation 2 Shimizu W : Gender difference and drug challenge in 2002 ; 106 : 2004 2011. brugada syndrome. J Cardiovasc Electrophysiol, 2004 ; 15 : 5 Matsuo K, Akahoshi M, Seto S, Yano K : Disappearance 70 71 of the brugada -type electrocardiogram after surgical 3 Chen Q, Kirsch GE, Zhang D, brugada R, brugada J, castration : a role for testosterone and an explanation brugada P, Potenza D, Moya A, Borggrefe M, for the male preponderance.

4 Pacing Clin Electrophysiol, Breithardt G, Ortiz-Lopez M, Wang Z, Antzelevitch C, 2003 ; 26 : 1551 1553. O'. Brien RE, Schulze-Bahr E, Keating MT, Towbin JA, JPN. J. ELECTROCARDIOLOGY Vol. 26 SUPPL. 4 2006 S-4-29.


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